Structural and functional characterization of chaperones in Fe-S cluster biogenesis and regulation
Dysfunctions in Fe-S protein biogenesis and mitochondrial iron accumulation in heart and neurones are part of the phenotype of a genetic neurodegenerative disease called Friedreich's ataxia. This pathology is caused by the deficiency of a mitochondrial protein, frataxin, highly conserved throug...
Main Author: | Puglisi, Rita |
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Other Authors: | Pastore, Annalisa |
Published: |
King's College London (University of London)
2017
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Online Access: | http://ethos.bl.uk/OrderDetails.do?uin=uk.bl.ethos.733341 |
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