Cellular and molecular characterisation of familial haemophagocytic lymphohistiocytosis type 1
Haemophagocytic lymphohistiocytosis (HLH) is a severe hyperinflammatory condition in which absent or markedly reduced T cell and natural killer (NK) cell cytotoxicity results in uncontrolled proliferation of T cells, activation of macrophages, hypercytokinaemia, pancytopaenia, and hepatosplenomegaly...
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Imperial College London
2011
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Online Access: | http://ethos.bl.uk/OrderDetails.do?uin=uk.bl.ethos.530262 |