Decreased outlet angle of the superior cerebellar artery as indicator for dolichoectasia in late onset Pompe disease

Decreased outlet angle of the superior cerebellar artery as indicator for dolichoectasia in late onset Pompe disease

Abstract Background Lysosomal α-glucosidase deficiency (Pompe disease) not only leads to glycogen accumulation in skeletal muscle, but also in the cerebral arteries. Dolichoectasia of the basilar artery (BA) has been frequently reported. Therefore progression of BA dolichoectasia in late onset Pompe...

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Bibliographic Details
Main Authors: Ole Hensel, Ilka Schneider, Mathias Wieprecht, Torsten Kraya, Stephan Zierz
Format: Article
Language:English
Published: BMC 2018-04-01
Series:Orphanet Journal of Rare Diseases
Subjects:
Late onset Pompe disease (LOPD)
Dolichoectasia of basilar artery
Dilative arteriopathy
Height of basilar bifurcation
Glycogenosis type II
Superior cerebellar artery (SUCA
Online Access:http://link.springer.com/article/10.1186/s13023-018-0794-6

Internet

http://link.springer.com/article/10.1186/s13023-018-0794-6

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