Matrix abnormalities in pulmonary fibrosis
Idiopathic pulmonary fibrosis (IPF) is a devastating, progressive disease, marked by excessive scarring, which leads to increased tissue stiffness, loss in lung function and ultimately death. IPF is characterised by progressive fibroblast and myofibroblast proliferation, and extensive deposition of...
| Main Authors: | , , , |
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| Format: | Article |
| Language: | English |
| Published: |
European Respiratory Society
2018-06-01
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| Series: | European Respiratory Review |
| Online Access: | http://err.ersjournals.com/content/27/148/180033.full |