Pycnodysostosis with Special Emphasis on Dentofacial Characteristics
Pycnodysostosis is an autosomal recessive disorder that manifests as osteosclerosis of the skeleton due to the defective osteoclasts mediated bone turnover. The diagnosis of this disorder is established on the basis of its characteristic features and must be differentially diagnosed with other bone...
Main Authors: | , , |
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Format: | Article |
Language: | English |
Published: |
Hindawi Limited
2015-01-01
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Series: | Case Reports in Dentistry |
Online Access: | http://dx.doi.org/10.1155/2015/817989 |