Quantitative muscle ultrasound and electrical impedance myography in late onset Pompe disease: A pilot study of reliability, longitudinal change and correlation with function

Quantitative muscle ultrasound and electrical impedance myography in late onset Pompe disease: A pilot study of reliability, longitudinal change and correlation with function

Background/objectives: Late-onset Pompe disease (LOPD) is slowly progressive, making it difficult to assess clinical change and response to interventions. In this study, quantitative muscle ultrasonography (QMUS) and electrical impedance myography (EIM) were evaluated as potential biomarkers. Method...

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Bibliographic Details
Main Authors: Lisa D. Hobson-Webb, Paul J. Zwelling, Shruti S. Raja, Ashley N. Pifer, Priya S. Kishnani
Format: Article
Language:English
Published: Elsevier 2021-09-01
Series:Molecular Genetics and Metabolism Reports
Subjects:
Muscle ultrasound
Neuromuscular ultrasound
Pompe disease
Late onset
Electrical impedance myography
Biomarker
Online Access:http://www.sciencedirect.com/science/article/pii/S2214426921000793

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http://www.sciencedirect.com/science/article/pii/S2214426921000793

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