Cryobiopsies are diagnostic in Pleuroparenchymal and Airway-centered Fibroelastosis

Abstract Background Idiopathic pulmonary fibroelastosis (iPPFE) is a rare lung lesion characterized by pleural and subpleural parenchymal thickening due to accumulation of fibroelastotic tissue. Only recently, a few cases with a peribronchiolar distribution of fibroelastotic tissue have been reporte...

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Bibliographic Details
Main Authors: Sissel Kronborg-White, Claudia Ravaglia, Alessandra Dubini, Sara Piciucchi, Sara Tomassetti, Elisabeth Bendstrup, Venerino Poletti
Format: Article
Language:English
Published: BMC 2018-07-01
Series:Respiratory Research
Subjects:
Online Access:http://link.springer.com/article/10.1186/s12931-018-0839-3