Pulmonary alveolar proteinosis

Pulmonary alveolar proteinosis (PAP) is a rare pulmonary disease characterised by alveolar accumulation of surfactant. It may result from mutations in surfactant proteins or granulocyte macrophage-colony stimulating factor (GM-CSF) receptor genes, it may be secondary to toxic inhalation or haematolo...

Full description

Bibliographic Details
Main Authors: B. Crestani, R. Epaud, M. Aubier, M-C. Dombret, C. Taille, M-P. Debray, C. Danel, R. Borie
Format: Article
Language:English
Published: European Respiratory Society 2011-06-01
Series:European Respiratory Review
Subjects:
Online Access:http://err.ersjournals.com/content/20/120/98.full.pdf+html