Quantification of Diaphragm Mechanics in Pompe Disease Using Dynamic 3D MRI.

Diaphragm weakness is the main reason for respiratory dysfunction in patients with Pompe disease, a progressive metabolic myopathy affecting respiratory and limb-girdle muscles. Since respiratory failure is the major cause of death among adult patients, early identification of respiratory muscle inv...

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Bibliographic Details
Main Authors: Katja Mogalle, Adria Perez-Rovira, Pierluigi Ciet, Stephan C A Wens, Pieter A van Doorn, Harm A W M Tiddens, Ans T van der Ploeg, Marleen de Bruijne
Format: Article
Language:English
Published: Public Library of Science (PLoS) 2016-01-01
Series:PLoS ONE
Online Access:http://europepmc.org/articles/PMC4938606?pdf=render