Schnitzler’s syndrome - a novel hypothesis of a shared pathophysiologic mechanism with Waldenström’s disease

Schnitzler’s syndrome - a novel hypothesis of a shared pathophysiologic mechanism with Waldenström’s disease

Abstract Schnitzler’s syndrome is an auto-inflammatory disorder which is characterized by two mandatory features: an urticarial rash and a monoclonal gammopathy. Although the pathophysiology of this syndrome is not yet fully understood, a role for interleukin-1 seems apparent. While this presumed li...

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Bibliographic Details
Main Authors: FS van Leersum, J Potjewijd, M van Geel, PM Steijlen, M Vreeburg
Format: Article
Language:English
Published: BMC 2019-06-01
Series:Orphanet Journal of Rare Diseases
Subjects:
Schnitzler’s syndrome
Waldenströms macroglobulinemia
Autoinflammatory disease
Hypothesis
Interleukin-1
MYD88
Online Access:http://link.springer.com/article/10.1186/s13023-019-1117-2

Internet

http://link.springer.com/article/10.1186/s13023-019-1117-2

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