A case of Alagille syndrome presenting with chronic cholestasis in an adult

A case of Alagille syndrome presenting with chronic cholestasis in an adult

Alagille syndrome (AGS) is a complex multisystem disorder that involves mainly the liver, heart, eyes, face, and skeleton. The main associated clinical features are chronic cholestasis due to a paucity of intrahepatic bile ducts, congenital heart disease primarily affecting pulmonary arteries, verte...

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Bibliographic Details
Main Authors: Jihye Kim, Bumhee Yang, Namyoung Paik, Yon Ho Choe, Yong-Han Paik
Format: Article
Language:English
Published: Korean Association for the Study of the Liver 2017-09-01
Series:Clinical and Molecular Hepatology
Subjects:
Alagille syndrome
Cholestasis
Bile-duct paucity
JAG1
Adult
Online Access:http://e-cmh.org/upload/pdf/cmh-2016-0057.pdf

Internet

http://e-cmh.org/upload/pdf/cmh-2016-0057.pdf

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