Perturbation of semaphorin and VEGF signaling in ACDMPV lungs due to FOXF1 deficiency

Perturbation of semaphorin and VEGF signaling in ACDMPV lungs due to FOXF1 deficiency

Abstract Background Alveolar capillary dysplasia with misalignment of pulmonary veins (ACDMPV) is a rare lethal congenital lung disorder in neonates characterized by severe progressive respiratory failure and refractory pulmonary hypertension, resulting from underdevelopment of the peripheral pulmon...

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Bibliographic Details
Main Authors: Justyna A. Karolak, Tomasz Gambin, Przemyslaw Szafranski, Rebecca L. Maywald, Edwina Popek, Jason D. Heaney, Paweł Stankiewicz
Format: Article
Language:English
Published: BMC 2021-07-01
Series:Respiratory Research
Subjects:
Plexins
Neuropilins
Vascular development
Lung branching
Lethal lung developmental disorders
Online Access:https://doi.org/10.1186/s12931-021-01797-7

Internet

https://doi.org/10.1186/s12931-021-01797-7

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