Neurodegeneration with Brain Iron Accumulation Disorders: Valuable Models Aimed at Understanding the Pathogenesis of Iron Deposition

by Sonia Levi, Valeria Tiranti
Published 2019-02-01

Neuroferritinopathy: From ferritin structure modification to pathogenetic mechanism

by Sonia Levi, Ermanna Rovida
Published 2015-09-01

Mitochondrial Ferritin: Its Role in Physiological and Pathological Conditions

by Sonia Levi, Maddalena Ripamonti, Marko Dardi, Anna Cozzi, Paolo Santambrogio
Published 2021-08-01

Characterization of the l-ferritin variant 460InsA responsible of a hereditary ferritinopathy disorder

by Anna Cozzi, Paolo Santambrogio, Barbara Corsi, Alessandro Campanella, Paolo Arosio, Sonia Levi
Published 2006-09-01

Oxidative stress and cell death in cells expressing L-ferritin variants causing neuroferritinopathy

by Anna Cozzi, Elisabetta Rovelli, Grazia Frizzale, Alessandro Campanella, Mario Amendola, Paolo Arosio, Sonia Levi
Published 2010-01-01

Mitochondrial iron and energetic dysfunction distinguish fibroblasts and induced neurons from pantothenate kinase-associated neurodegeneration patients

by Paolo Santambrogio, Sabrina Dusi, Michela Guaraldo, Luisa Ida Rotundo, Vania Broccoli, Barbara Garavaglia, Valeria Tiranti, Sonia Levi
Published 2015-09-01

Neuronal Ablation of CoA Synthase Causes Motor Deficits, Iron Dyshomeostasis, and Mitochondrial Dysfunctions in a CoPAN Mouse Model

by Ivano Di Meo, Chiara Cavestro, Silvia Pedretti, Tingting Fu, Simona Ligorio, Antonello Manocchio, Lucrezia Lavermicocca, Paolo Santambrogio, Maddalena Ripamonti, Sonia Levi, Sophie Ayciriex, Nico Mitro, Valeria Tiranti
Published 2020-12-01

Harmful Iron-Calcium Relationship in Pantothenate kinase Associated Neurodegeneration

by Paolo Santambrogio, Maddalena Ripamonti, Chiara Paolizzi, Celeste Panteghini, Miryam Carecchio, Luisa Chiapparini, Marzia Raimondi, Alicia Rubio, Ivano Di Meo, Anna Cozzi, Stefano Taverna, Giuseppe De Palma, Valeria Tiranti, Sonia Levi
Published 2020-05-01

The pathogenesis of cardiomyopathy in Friedreich ataxia.

by Arnulf H Koeppen, R Liane Ramirez, Alyssa B Becker, Sarah T Bjork, Sonia Levi, Paolo Santambrogio, Patrick J Parsons, Pamela C Kruger, Karl X Yang, Paul J Feustel, Joseph E Mazurkiewicz
Published 2015-01-01

A novel neuroferritinopathy mouse model (FTL 498InsTC) shows progressive brain iron dysregulation, morphological signs of early neurodegeneration and motor coordination deficits

by Federica Maccarinelli, Antonella Pagani, Anna Cozzi, Franca Codazzi, Giuseppina Di Giacomo, Sara Capoccia, Stefania Rapino, Dario Finazzi, Letterio Salvatore Politi, Francesca Cirulli, Marco Giorgio, Ottavio Cremona, Fabio Grohovaz, Sonia Levi
Published 2015-09-01

Stem Cell Modeling of Neuroferritinopathy Reveals Iron as a Determinant of Senescence and Ferroptosis during Neuronal Aging

by Anna Cozzi, Daniel I. Orellana, Paolo Santambrogio, Alicia Rubio, Cinzia Cancellieri, Serena Giannelli, Maddalena Ripamonti, Stefano Taverna, Giulia Di Lullo, Ermanna Rovida, Maurizio Ferrari, Gian Luca Forni, Chiara Fiorillo, Vania Broccoli, Sonia Levi
Published 2019-11-01

Data demonstrating the role of peroxiredoxin 2 as important anti-oxidant system in lung homeostasis

by Enrica Federti, Alessandro Matte, Alessandra Ghigo, Immacolata Andolfo, Cimino James, Angela Siciliano, Christophe Leboeuf, Anne Janin, Francesco Manna, Soo Young Choi, Achille Iolascon, Elisabetta Beneduce, Davide Melisi, Dae Won Kim, Sonia Levi, Lucia De Franceschi
Published 2017-12-01