Flavin adenine dinucleotide rescues the phenotype of frataxin deficiency.

by Pilar Gonzalez-Cabo, Sheila Ros, Francesc Palau
Published 2010-01-01

The Role of Iron in Friedreich’s Ataxia: Insights From Studies in Human Tissues and Cellular and Animal Models

by José Vicente Llorens, José Vicente Llorens, Sirena Soriano, Sirena Soriano, Pablo Calap-Quintana, Pablo Calap-Quintana, Pilar Gonzalez-Cabo, Pilar Gonzalez-Cabo, Pilar Gonzalez-Cabo, María Dolores Moltó, María Dolores Moltó, María Dolores Moltó
Published 2019-02-01

Much More Than a Scaffold: Cytoskeletal Proteins in Neurological Disorders

by Diana C. Muñoz-Lasso, Carlos Romá-Mateo, Federico V. Pallardó, Pilar Gonzalez-Cabo
Published 2020-02-01

Thioredoxin and Glutaredoxin Systems as Potential Targets for the Development of New Treatments in Friedreich’s Ataxia

by Marta Seco-Cervera, Pilar González-Cabo, Federico V. Pallardó, Carlos Romá-Mateo, José Luis García-Giménez
Published 2020-12-01

Two different pathogenic mechanisms, dying-back axonal neuropathy and pancreatic senescence, are present in the YG8R mouse model of Friedreich’s ataxia

by Belén Mollá, Fátima Riveiro, Arantxa Bolinches-Amorós, Diana C. Muñoz-Lasso, Francesc Palau, Pilar González-Cabo
Published 2016-06-01

Cofilin and Neurodegeneration: New Functions for an Old but Gold Protein

by Tamara Lapeña-Luzón, Laura R. Rodríguez, Vicent Beltran-Beltran, Noelia Benetó, Federico V. Pallardó, Pilar Gonzalez-Cabo
Published 2021-07-01

Antioxidant Therapies and Oxidative Stress in Friedreich´s Ataxia: The Right Path or Just a Diversion?

by Laura R. Rodríguez, Tamara Lapeña, Pablo Calap-Quintana, María Dolores Moltó, Pilar Gonzalez-Cabo, Juan Antonio Navarro Langa
Published 2020-07-01

Oxidative stress modulates rearrangement of endoplasmic reticulum-mitochondria contacts and calcium dysregulation in a Friedreich's ataxia model

by Laura R. Rodríguez, Pablo Calap-Quintana, Tamara Lapeña-Luzón, Federico V. Pallardó, Stephan Schneuwly, Juan A. Navarro, Pilar Gonzalez-Cabo
Published 2020-10-01

Differential expression of PGC-1α and metabolic sensors suggest age-dependent induction of mitochondrial biogenesis in Friedreich ataxia fibroblasts.

by José Luis García-Giménez, Amparo Gimeno, Pilar Gonzalez-Cabo, Francisco Dasí, Arantxa Bolinches-Amorós, Belén Mollá, Francesc Palau, Federico V Pallardó
Published 2011-01-01

Cofilin dysregulation alters actin turnover in frataxin-deficient neurons

by Diana C. Muñoz-Lasso, Belén Mollá, Pablo Calap-Quintana, José Luis García-Giménez, Federico V. Pallardo, Francesc Palau, Pilar Gonzalez-Cabo
Published 2020-03-01

Reversible Axonal Dystrophy by Calcium Modulation in Frataxin-Deficient Sensory Neurons of YG8R Mice

by Belén Mollá, Belén Mollá, Diana C. Muñoz-Lasso, Diana C. Muñoz-Lasso, Diana C. Muñoz-Lasso, Diana C. Muñoz-Lasso, Fátima Riveiro, Fátima Riveiro, Arantxa Bolinches-Amorós, Arantxa Bolinches-Amorós, Federico V. Pallardó, Federico V. Pallardó, Federico V. Pallardó, Angel Fernandez-Vilata, María de la Iglesia-Vaya, María de la Iglesia-Vaya, María de la Iglesia-Vaya, Francesc Palau, Francesc Palau, Francesc Palau, Pilar Gonzalez-Cabo, Pilar Gonzalez-Cabo, Pilar Gonzalez-Cabo
Published 2017-08-01

PPAR gamma agonist leriglitazone improves frataxin-loss impairments in cellular and animal models of Friedreich Ataxia

by Laura Rodríguez-Pascau, Elena Britti, Pablo Calap-Quintana, Yi Na Dong, Cristina Vergara, Fabien Delaspre, Marta Medina-Carbonero, Jordi Tamarit, Federico V. Pallardó, Pilar Gonzalez-Cabo, Joaquim Ros, David R. Lynch, Marc Martinell, Pilar Pizcueta
Published 2021-01-01