Aggresome Formation in Neuropathy Models Based on Peripheral Myelin Protein 22 Mutations

by Mary C. Ryan, Eric M. Shooter, Lucia Notterpek
Published 2002-07-01

Inducible HSP70 Is Critical in Preventing the Aggregation and Enhancing the Processing of PMP22

by Vinita G. Chittoor-Vinod, Sooyeon Lee, Sarah M. Judge, Lucia Notterpek
Published 2015-02-01

PMP22 Accumulation in Aggresomes: Implications for CMT1A Pathology

by Lucia Notterpek, Mary C. Ryan, Andreas R. Tobler, Eric M. Shooter
Published 1999-10-01

Pharmacological induction of the heat shock response improves myelination in a neuropathic model

by Sunitha Rangaraju, Irina Madorsky, Jocelyn Go Pileggi, Adeela Kamal, Lucia Notterpek
Published 2008-10-01

Liposomes to target peripheral neurons and Schwann cells.

by Sooyeon Lee, Ana Tari Ashizawa, Kwang Sik Kim, Darin J Falk, Lucia Notterpek
Published 2013-01-01

The formation of peripheral myelin protein 22 aggregates is hindered by the enhancement of autophagy and expression of cytoplasmic chaperones

by Jenny Fortun, Jonathan D. Verrier, Jocelyn C. Go, Irina Madorsky, William A. Dunn, Lucia Notterpek
Published 2007-02-01

Alterations in degradative pathways and protein aggregation in a neuropathy model based on PMP22 overexpression

by Jenny Fortun, Jocelyn C. Go, Jie Li, Stephanie A. Amici, William A. Dunn, Jr., Lucia Notterpek
Published 2006-04-01

The Palmitoylation State of PMP22 Modulates Epithelial Cell Morphology and Migration

by Susie J. Zoltewicz, Sooyeon Lee, Vinita G. Chittoor, Steven M. Freeland, Sunitha Rangaraju, David A. Zacharias, Lucia Notterpek
Published 2012-11-01

Biochemical Characterization of Protein Quality Control Mechanisms during Disease Progression in the C22 Mouse Model of CMT1A

by Vinita G. Chittoor, Lee Sooyeon, Sunitha Rangaraju, Jessica R. Nicks, Jordan T. Schmidt, Irina Madorsky, Diana C. Narvaez, Lucia Notterpek
Published 2013-10-01

Intermittent fasting alleviates the neuropathic phenotype in a mouse model of Charcot–Marie–Tooth disease

by Irina Madorsky, Katherine Opalach, Amanda Waber, Jonathan D. Verrier, Chelsea Solmo, Thomas Foster, William A. Dunn, Jr., Lucia Notterpek
Published 2009-04-01

Rapamycin improves peripheral nerve myelination while it fails to benefit neuromuscular performance in neuropathic mice

by Jessica Nicks, Sooyeon Lee, Andrew Harris, Darin J. Falk, Adrian G. Todd, Karla Arredondo, William A. Dunn, Jr., Lucia Notterpek
Published 2014-10-01

Retraction Note: Transgenic mice overexpressing the ALS-linked protein Matrin 3 develop a profound muscle phenotype

by Christina Moloney, Sruti Rayaprolu, John Howard, Susan Fromholt, Hilda Brown, Matt Collins, Mariela Cabrera, Colin Duffy, Zoe Siemienski, Dave Miller, Maurice S. Swanson, Lucia Notterpek, David R. Borchelt, Jada Lewis
Published 2017-12-01

A brief review of recent Charcot-Marie-Tooth research and priorities [v1; ref status: indexed, http://f1000r.es/53g]

by Sean Ekins, Nadia K. Litterman, Renée J.G. Arnold, Robert W. Burgess, Joel S. Freundlich, Steven J. Gray, Joseph J. Higgins, Brett Langley, Dianna E. Willis, Lucia Notterpek, David Pleasure, Michael W. Sereda, Allison Moore
Published 2015-02-01