Identification des mécanismes physiopathologiques de la dystrophie facioscapulohumérale : rôle de la mitochondrie et du stress oxydant

Identification des mécanismes physiopathologiques de la dystrophie facioscapulohumérale : rôle de la mitochondrie et du stress oxydant

La dystrophie facioscapulohumérale (FSHD) est une dystrophie musculaire autosomique dominante, dégénérative et progressive. Les traitements élaborés jusqu'à présent n'ont pas réussi à améliorer le quotidien des patients FSHD. Plusieurs études se sont focalisées sur les mécanismes moléculai...

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Bibliographic Details
Main Author:	Turki, Ahmed
Other Authors:	Montpellier 1
Language:	fr
Published:	2012
Subjects:	Dystrophie facioscapulohumérale Mécanismes physiopathologiques Mitochondrie Stress oxydant Facioscapulohumeral muscular dystrophy Patho-physiological mecanisms Mitochondria Oxidant stress
Online Access:	http://www.theses.fr/2012MON1T024

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