Pulmonary hypertension in children and young adults with sickle cell disease

INTRODUCTION: Primary pulmonary hypertension (PH) is a progressive disease that is characterized by restricted blood flow in the pulmonary vasculature, resulting in an increase in pulmonary vascular resistance (PVR) (McLaughlin et al., 2009). Patients with sickle cell disease (SCD), a monogenic bloo...

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Bibliographic Details
Main Author: Sheppard, Kristin
Language:en_US
Published: 2016
Subjects:
Online Access:https://hdl.handle.net/2144/17027