The biochemical basis of congenital disorders of glycosylation
The enzyme peptide: N-glycanase (EC 3.5.1.52) is an endoglycosidase which cleaves N-linked glycans from incorrectly folded glycoproteins exported from the endoplasmic reticulum during ER-associated degradation (ERAD). Clinical mutations in this enzyme (resulting in loss or decrease in function) are...
Main Author: | Needs, Sarah |
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Published: |
Open University
2018
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Online Access: | https://ethos.bl.uk/OrderDetails.do?uin=uk.bl.ethos.765592 |
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