Frantz' tumour: a rare pancreatic neoplasm

Frantz' tumour of the pancreas is also known as solid pseudopapillary tumour (SPT) of the pancreas. It is a rare pancreatic neoplasm and represents about 3% of all the pancreatic cystic neoplasm. It occurs predominantly in young woman in 2nd to 3rd decade of life. These tumours exhibit indolent...

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Bibliographic Details
Main Authors: Ikhwan Sani Mohamad (Author), Boo, HS (Author), Zamri Zainal (Author), Affirul C (Author), Razman Jarmin (Author)
Format: Article
Language:English
Published: Pusat Perubatan Universiti Kebangsaan Malaysia, 2017.
Online Access:Get fulltext
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100 1 0 |a Ikhwan Sani Mohamad,   |e author 
700 1 0 |a Boo, HS  |e author 
700 1 0 |a Zamri Zainal,   |e author 
700 1 0 |a Affirul C,   |e author 
700 1 0 |a Razman Jarmin,   |e author 
245 0 0 |a Frantz' tumour: a rare pancreatic neoplasm 
260 |b Pusat Perubatan Universiti Kebangsaan Malaysia,   |c 2017. 
856 |z Get fulltext  |u http://journalarticle.ukm.my/12269/1/8._ikhwan_et_al.pdf 
520 |a Frantz' tumour of the pancreas is also known as solid pseudopapillary tumour (SPT) of the pancreas. It is a rare pancreatic neoplasm and represents about 3% of all the pancreatic cystic neoplasm. It occurs predominantly in young woman in 2nd to 3rd decade of life. These tumours exhibit indolent behaviour and very often reach considerable size before the first symptoms appear. Despite this presentation these tumours have low malignant potential and complete surgical resection render excellent prognosis. We reported a case of a 16-year-old girl who presented with upper abdominal mass with symptoms of gastric outlet obstruction for 7 months duration. Clinical examination revealed a huge epigastric mass measuring 10 x 12 cm in size. CT scan showed presence of mass arising from the body of the pancreas which was hypervascular, well-encapsulated with mixed cystic and solid components. She then underwent successful distal pancreatectomy and splenectomy and recovered uneventfully. 
546 |a en