Polysplenia syndrome with situs ambiguous, common mesentery, and IVC interruption discovered incidentally in an adult

Polysplenia syndrome associates multiple spleens to other malformations, most frequently cardiac, vascular, visceral, and biliary malformations. Polysplenia has been described mainly in childhood owing to critical anatomic malformations related to cardiac defects or biliary atresia. We present a cas...

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Main Authors: Hajar El Mortaji, Kenza Elatiqi, Hanane El Hammaoui, Soumaya Alj
Format: Article
Language:English
Published: Elsevier 2019-09-01
Series:Radiology Case Reports
Online Access:http://www.sciencedirect.com/science/article/pii/S1930043319301682
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spelling doaj-fa353490b9a64e0b97cca3babd830ee22020-11-25T00:25:36ZengElsevierRadiology Case Reports1930-04332019-09-0114910721075Polysplenia syndrome with situs ambiguous, common mesentery, and IVC interruption discovered incidentally in an adultHajar El Mortaji0Kenza Elatiqi1Hanane El Hammaoui2Soumaya Alj3Corresponding author.; Department of Radiology, Ibn Tofail Hospital, Med VI University Center, Marrakech, MoroccoDepartment of Radiology, Ibn Tofail Hospital, Med VI University Center, Marrakech, MoroccoDepartment of Radiology, Ibn Tofail Hospital, Med VI University Center, Marrakech, MoroccoDepartment of Radiology, Ibn Tofail Hospital, Med VI University Center, Marrakech, MoroccoPolysplenia syndrome associates multiple spleens to other malformations, most frequently cardiac, vascular, visceral, and biliary malformations. Polysplenia has been described mainly in childhood owing to critical anatomic malformations related to cardiac defects or biliary atresia. We present a case of polysplenia syndrome found in a 58-year-old man. Only those with mild anatomical abnormalities reach adulthood without a diagnosis. Radiological examinations are helpful to the diagnosis by ascertaining the location and number of spleens, location of other organs in the chest and abdomen, and identification of other associated anomalies. Keywords: Polysplenia syndrome, Heterotaxy, Common mesentery, Splenic cysts, IVC interruptionhttp://www.sciencedirect.com/science/article/pii/S1930043319301682
collection DOAJ
language English
format Article
sources DOAJ
author Hajar El Mortaji
Kenza Elatiqi
Hanane El Hammaoui
Soumaya Alj
spellingShingle Hajar El Mortaji
Kenza Elatiqi
Hanane El Hammaoui
Soumaya Alj
Polysplenia syndrome with situs ambiguous, common mesentery, and IVC interruption discovered incidentally in an adult
Radiology Case Reports
author_facet Hajar El Mortaji
Kenza Elatiqi
Hanane El Hammaoui
Soumaya Alj
author_sort Hajar El Mortaji
title Polysplenia syndrome with situs ambiguous, common mesentery, and IVC interruption discovered incidentally in an adult
title_short Polysplenia syndrome with situs ambiguous, common mesentery, and IVC interruption discovered incidentally in an adult
title_full Polysplenia syndrome with situs ambiguous, common mesentery, and IVC interruption discovered incidentally in an adult
title_fullStr Polysplenia syndrome with situs ambiguous, common mesentery, and IVC interruption discovered incidentally in an adult
title_full_unstemmed Polysplenia syndrome with situs ambiguous, common mesentery, and IVC interruption discovered incidentally in an adult
title_sort polysplenia syndrome with situs ambiguous, common mesentery, and ivc interruption discovered incidentally in an adult
publisher Elsevier
series Radiology Case Reports
issn 1930-0433
publishDate 2019-09-01
description Polysplenia syndrome associates multiple spleens to other malformations, most frequently cardiac, vascular, visceral, and biliary malformations. Polysplenia has been described mainly in childhood owing to critical anatomic malformations related to cardiac defects or biliary atresia. We present a case of polysplenia syndrome found in a 58-year-old man. Only those with mild anatomical abnormalities reach adulthood without a diagnosis. Radiological examinations are helpful to the diagnosis by ascertaining the location and number of spleens, location of other organs in the chest and abdomen, and identification of other associated anomalies. Keywords: Polysplenia syndrome, Heterotaxy, Common mesentery, Splenic cysts, IVC interruption
url http://www.sciencedirect.com/science/article/pii/S1930043319301682
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