Polysplenia syndrome with situs ambiguous, common mesentery, and IVC interruption discovered incidentally in an adult
Polysplenia syndrome associates multiple spleens to other malformations, most frequently cardiac, vascular, visceral, and biliary malformations. Polysplenia has been described mainly in childhood owing to critical anatomic malformations related to cardiac defects or biliary atresia. We present a cas...
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2019-09-01
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Series: | Radiology Case Reports |
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doaj-fa353490b9a64e0b97cca3babd830ee22020-11-25T00:25:36ZengElsevierRadiology Case Reports1930-04332019-09-0114910721075Polysplenia syndrome with situs ambiguous, common mesentery, and IVC interruption discovered incidentally in an adultHajar El Mortaji0Kenza Elatiqi1Hanane El Hammaoui2Soumaya Alj3Corresponding author.; Department of Radiology, Ibn Tofail Hospital, Med VI University Center, Marrakech, MoroccoDepartment of Radiology, Ibn Tofail Hospital, Med VI University Center, Marrakech, MoroccoDepartment of Radiology, Ibn Tofail Hospital, Med VI University Center, Marrakech, MoroccoDepartment of Radiology, Ibn Tofail Hospital, Med VI University Center, Marrakech, MoroccoPolysplenia syndrome associates multiple spleens to other malformations, most frequently cardiac, vascular, visceral, and biliary malformations. Polysplenia has been described mainly in childhood owing to critical anatomic malformations related to cardiac defects or biliary atresia. We present a case of polysplenia syndrome found in a 58-year-old man. Only those with mild anatomical abnormalities reach adulthood without a diagnosis. Radiological examinations are helpful to the diagnosis by ascertaining the location and number of spleens, location of other organs in the chest and abdomen, and identification of other associated anomalies. Keywords: Polysplenia syndrome, Heterotaxy, Common mesentery, Splenic cysts, IVC interruptionhttp://www.sciencedirect.com/science/article/pii/S1930043319301682 |
collection |
DOAJ |
language |
English |
format |
Article |
sources |
DOAJ |
author |
Hajar El Mortaji Kenza Elatiqi Hanane El Hammaoui Soumaya Alj |
spellingShingle |
Hajar El Mortaji Kenza Elatiqi Hanane El Hammaoui Soumaya Alj Polysplenia syndrome with situs ambiguous, common mesentery, and IVC interruption discovered incidentally in an adult Radiology Case Reports |
author_facet |
Hajar El Mortaji Kenza Elatiqi Hanane El Hammaoui Soumaya Alj |
author_sort |
Hajar El Mortaji |
title |
Polysplenia syndrome with situs ambiguous, common mesentery, and IVC interruption discovered incidentally in an adult |
title_short |
Polysplenia syndrome with situs ambiguous, common mesentery, and IVC interruption discovered incidentally in an adult |
title_full |
Polysplenia syndrome with situs ambiguous, common mesentery, and IVC interruption discovered incidentally in an adult |
title_fullStr |
Polysplenia syndrome with situs ambiguous, common mesentery, and IVC interruption discovered incidentally in an adult |
title_full_unstemmed |
Polysplenia syndrome with situs ambiguous, common mesentery, and IVC interruption discovered incidentally in an adult |
title_sort |
polysplenia syndrome with situs ambiguous, common mesentery, and ivc interruption discovered incidentally in an adult |
publisher |
Elsevier |
series |
Radiology Case Reports |
issn |
1930-0433 |
publishDate |
2019-09-01 |
description |
Polysplenia syndrome associates multiple spleens to other malformations, most frequently cardiac, vascular, visceral, and biliary malformations. Polysplenia has been described mainly in childhood owing to critical anatomic malformations related to cardiac defects or biliary atresia. We present a case of polysplenia syndrome found in a 58-year-old man. Only those with mild anatomical abnormalities reach adulthood without a diagnosis. Radiological examinations are helpful to the diagnosis by ascertaining the location and number of spleens, location of other organs in the chest and abdomen, and identification of other associated anomalies. Keywords: Polysplenia syndrome, Heterotaxy, Common mesentery, Splenic cysts, IVC interruption |
url |
http://www.sciencedirect.com/science/article/pii/S1930043319301682 |
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