Double valve replacement in a patient with Maroteaux – Lamy syndrome as an ultimate team challenge

Abstract Background The Maroteaux-Lamy syndrome (Mucopolysaccharidosis type VI) is a rare, inherited metabolic disease that results in progressive tissue accumulation of dermatan-sulfated glycosaminoglycans and inflammatory consequences that almost always affects the heart valves. From the anesthesi...

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Bibliographic Details
Main Authors: Alexandros Agron Demis, Stella Oikonomidou, Fotios Daglis, Spyridon Polymenakos, Matthew Panagiotou
Format: Article
Language:English
Published: BMC 2021-05-01
Series:Journal of Cardiothoracic Surgery
Subjects:
Online Access:https://doi.org/10.1186/s13019-021-01530-x