Anesthetic management of a pediatric patient with hypohidrotic ectodermal dysplasia undergoing emergency surgery

• Main Authors: Elif Oral Ahiskalioglu, Ali Ahiskalioglu, Binali Firinci, Aysenur Dostbil, Mehmet Aksoy
• Format: Article
• Language: English
• Published: Elsevier 2015-11-01
• Series: Brazilian Journal of Anesthesiology
• Subjects: Ectodermal dysplasia; Regional anesthesia; Acute abdomen
• Online Access: http://www.sciencedirect.com/science/article/pii/S0104001413002327

Ectodermal dysplasias are rare conditions with a triad of hypotrichosis, anodontia and anhidrosis. In literature review there have been only a few reports of anesthetic management of patients with ectodermal dysplasias. Hyperthermia is a very serious risk which may occur due to the defect of sweat glands. The present case involves a 10-year-old child with ectodermal dysplasia who presented with an acute abdomen and was considered for an emergency surgery. Our aim was to demonstrate the successful management of this case using a combination of general and epidural anesthesia. It is important for anesthesiologist to have information about this syndrome in case of emergency operations, since it can prevent serious complications and even save lives.