Targeted metabolomic analyses of cellular models of pelizaeus-merzbacher disease reveal plasmalogen and myo-inositol solute carrier dysfunction
<p>Abstract</p> <p>Background</p> <p>Leukodystrophies are devastating diseases characterized by dys- and hypo-myelination. While there are a number of histological and imaging studies of these disorders, there are limited biochemical data available. We undertook targete...
Main Authors: | Pelzer Lindsay, Smith Tara, Wood Paul L, Goodenowe Dayan B |
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Format: | Article |
Language: | English |
Published: |
BMC
2011-06-01
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Series: | Lipids in Health and Disease |
Subjects: | |
Online Access: | http://www.lipidworld.com/content/10/1/102 |
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