Cor triatriatum and lipomatous hypertrophy of the interatrial septum in the elderly: a case report

<p>Abstract</p> <p>Cor triatriatum is a rare congenital heart defect characterized by the presence of a fibromuscular membrane dividing the left atrium into two distinct chambers. Lipomatous hypertrophy of the atrial septum is an infrequently observed benign abnormality caused by l...

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Bibliographic Details
Main Authors: Mercuro Giuseppe, Tumbarello Roberto, Bassareo Pier
Format: Article
Language:English
Published: BMC 2010-03-01
Series:Cardiovascular Ultrasound
Online Access:http://www.cardiovascularultrasound.com/content/8/1/4
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Summary:<p>Abstract</p> <p>Cor triatriatum is a rare congenital heart defect characterized by the presence of a fibromuscular membrane dividing the left atrium into two distinct chambers. Lipomatous hypertrophy of the atrial septum is an infrequently observed benign abnormality caused by large fatty tissue deposits in the interatrial septum. An increased incidence of atrial arrhythmias is described in both pathologies, while a significant obstruction of blood flow mimicking mitral stenosis is typically manifested in cor triatriatum. We report the case of a 75-year-old woman with a previously undescribed association of the above stated abnormalities detected by both transthoracic and transeosophageal echocardiography. Diagnosis was confirmed by means of computed tomography. The singular physiologic and anatomic factors underlying survival until such a late age are described. The diagnostic, therapeutic and surgical management is discussed and a short review of the literature performed.</p>
ISSN:1476-7120