Anti-nuclear antibody-negative immunoglobulin G4-associated autoimmune hepatitis mimicking lymphoproliferative disorders

Anti-nuclear antibody-negative immunoglobulin G4-associated autoimmune hepatitis mimicking lymphoproliferative disorders

Immunoglobulin G4 (IgG4)-associated autoimmune hepatitis (AIH) is a very rare subtype of autoimmune hepatitis and characterized by marked elevated serum IgG and hepatic infiltration of IgG4-expressing plasma cells. Pathologic confirmation of hepatic IgG4-expressing plasma cells is usually required f...

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Bibliographic Details
Main Authors: Min Kyu Kang, Jung Gil Park, Joon Hyuk Choi
Format: Article
Language:English
Published: Yeungnam University College of Medicine 2020-04-01
Series:Yeungnam University Journal of Medicine
Subjects:
autoimmune hepatitis
immunoglobulin g
immunoglobulin g4-related disease
plasma cells
prednisolone
Online Access:http://www.e-yujm.org/upload/pdf/yujm-2020-00066.pdf
Description
Summary:Immunoglobulin G4 (IgG4)-associated autoimmune hepatitis (AIH) is a very rare subtype of autoimmune hepatitis and characterized by marked elevated serum IgG and hepatic infiltration of IgG4-expressing plasma cells. Pathologic confirmation of hepatic IgG4-expressing plasma cells is usually required for the final diagnosis of IgG4-associated AIH. Herein, we report the case of a 47-year-old female diagnosed with autoantibody-negative IgG4-associated AIH mimicking lymphoproliferative disorders.
ISSN:2384-0293

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