Splenic rupture and intracranial haemorrhage in a haemophilic neonate: Case report and literature review

• Main Authors: Ibrahim Adamu, Armand Asarian, Philip Xiao
• Format: Article
• Language: English
• Published: Wolters Kluwer Medknow Publications 2012-01-01
• Series: African Journal of Paediatric Surgery
• Subjects: Hemophilia; intracranial hemorrhage; neonate; splenic rupture
• Online Access: http://www.afrjpaedsurg.org/article.asp?issn=0189-6725;year=2012;volume=9;issue=2;spage=163;epage=165;aulast=Adamu
• ISSN: 0189-6725; 0974-5998

Splenic rupture and intracranial haemorrhage are life-threatening conditions infrequently encountered in neonates without history of birth trauma. External manifestations of birth trauma; namely, capput succadeneum and cephalhematoma, when present raise suspicions for more serious intracranial or visceral damage. Rupture of normal spleen without an obvious source of trauma in haemophilic neonate is a rare event. The concurrence of both conditions and the unusual presentation make this case a rare one that is seldom encountered in the literature. Additionally, when splenic rupture occurs, the consensus is to employ all non-operative techniques aimed at salvaging the spleen, thus avoiding the immune-compromised state associated with splenectomy. However, in this case, we present a 3-day-old male with family history of haemophilia A, who was diagnosed with splenic rupture and bilateral subdural haematomas and underwent splenectomy, albeit with post-operative complications, in light of haemodynamic instability and high ongoing transfusion requirements.