Peutz-Jeghers Syndrome Report of one case associated with Gastrointestin Carcinoma

The peutz-Jeghers syndrome is characterized by an association of gastrointestinal polyposis with rnelain spots on oral mucosa, lips, and skin. This symdrorne is inherited as a simple mendelian autosomal dominant trait. Intussusception is by far the most common complication. Although these polyps ar...

Full description

Bibliographic Details
Main Authors: SHARIAT F., SHAMIMI K.
Format: Article
Language:English
Published: Tehran University of Medical Sciences 1982-12-01
Series:Acta Medica Iranica
Online Access:https://acta.tums.ac.ir/index.php/acta/article/view/167
Description
Summary:The peutz-Jeghers syndrome is characterized by an association of gastrointestinal polyposis with rnelain spots on oral mucosa, lips, and skin. This symdrorne is inherited as a simple mendelian autosomal dominant trait. Intussusception is by far the most common complication. Although these polyps are widely regarded as hamartomas and rarely undergo malignant change, they have been reported to be associated with carcinoma of gastrointestin and ovary. In the case reported here, the cancer developed from hamartomatous polyps.
ISSN:0044-6025
1735-9694