CONGENITAL SELF HEALING CUTANEOUS LANGERHANS CELL HISTIOCYTOSIS WITH MULTIPLE HYPOPIGMENTED MACULES AFTER RECOVERY IN A NEONATE

CONGENITAL SELF HEALING CUTANEOUS LANGERHANS CELL HISTIOCYTOSIS WITH MULTIPLE HYPOPIGMENTED MACULES AFTER RECOVERY IN A NEONATE

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Langerhans cell histiocytosis (LCH) is the most common type of childhood histiocytic disorder with an incidence of 0.2 to 1 per 100,000 children under the age of 15 years (1). The clinical picture of LCH varies from single system (S-S)bone or skin disease to multi-system disease (M-S) (2). We repor...

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Bibliographic Details
Main Authors: A. Ramyar, B. Yaghmaie M. Monajemzadeh
Format: Article
Language:English
Published: Tehran University of Medical Sciences 2008-02-01
Series:Acta Medica Iranica
Subjects:
Congenital self healing langerhans cell histiocytosis (CSHLCH)
Langerhans cell histiocytosis (LCH)
Hashimato Pritzker disease
Online Access:https://acta.tums.ac.ir/index.php/acta/article/view/3448
Description
Summary:Langerhans cell histiocytosis (LCH) is the most common type of childhood histiocytic disorder with an incidence of 0.2 to 1 per 100,000 children under the age of 15 years (1). The clinical picture of LCH varies from single system (S-S)bone or skin disease to multi-system disease (M-S) (2). We report a neonate with disseminated papulonodular eruption containing mononuclear CD1a and S100 positive histiocytic cells infiltration at epidermis and underlying dermis. The diagnosis of a congenital self healing Langerhans cell histiocytosis (CSHLCH) was made and follow up showed a complete recovery of the eruptions , leaving hypopigmented macules in the sites corresponding to the initial findings.
ISSN:0044-6025
1735-9694

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