Anaesthetic considerations for liver transplantation in propionic acidemia

Anaesthetic considerations for liver transplantation in propionic acidemia

Propionic acidemia (PA) is an autosomal recessive disorder of metabolism due to deficiency of the enzyme propionyl-CoA carboxylase (PCC) that converts propionyl-CoA to methylmalonyl-CoA with the help of the cofactor biotin inside the mitochondria. The resultant accumulation of propionyl-CoA causes s...

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Bibliographic Details
Main Authors: Akila Rajakumar, Ilankumaran Kaliamoorthy, Mettu Srinivas Reddy, Mohamed Rela
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2016-01-01
Series:Indian Journal of Anaesthesia
Subjects:
Hyperammonaemic crisis, inborn metabolic errors, liver transplantation, organic acidemia, propionic acidemia and anaesthesia
Online Access:http://www.ijaweb.org/article.asp?issn=0019-5049;year=2016;volume=60;issue=1;spage=50;epage=54;aulast=Rajakumar

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http://www.ijaweb.org/article.asp?issn=0019-5049;year=2016;volume=60;issue=1;spage=50;epage=54;aulast=Rajakumar

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