Hirayama disease

Hirayama disease

Hirayama disease (HD) is a rare cause of cervical myelopathy often misdiagnosed as motor neuron disease and easily missed on routine magnetic resonance imaging (MRI), at time where detection is crucial to prevent irreversible cord injury. Believed to be a cervical flexion myelopathy, HD differs from...

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Main Authors: Chanabasappa V. Chavadi, Gowtham Jasti, Madhav Hegde, Anand Venugopal
Format: Article
Language:English
Published: Thieme Medical Publishers, Inc. 2014-05-01
Series:Indian Journal of Neurosurgery
Subjects:
cervical myelopathy
hand wasting
hirayama disease
magnetic resonance imaging
Online Access:http://www.thieme-connect.de/DOI/DOI?10.4103/2277-9167.138924
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spelling doaj-e2d6422077914d03a2aa81e7dc9384182020-11-25T03:21:34ZengThieme Medical Publishers, Inc.Indian Journal of Neurosurgery2277-954X2277-91672014-05-01030212512710.4103/2277-9167.138924Hirayama diseaseChanabasappa V. ChavadiGowtham JastiMadhav Hegde0Anand VenugopalAmbedkar Medical CollegeHirayama disease (HD) is a rare cause of cervical myelopathy often misdiagnosed as motor neuron disease and easily missed on routine magnetic resonance imaging (MRI), at time where detection is crucial to prevent irreversible cord injury. Believed to be a cervical flexion myelopathy, HD differs from motor neuron diseases because of its nonprogressive course and pathologic findings of chronic microcirculatory changes in the lower cervical cord. Dynamic forward displacement of dura in flexion causes asymmetric flattening of lower cervical cord. While dynamic contrast MRI is diagnostic, routine study has high predictive value. A case of HD, etiopathogenesis, imaging and treatment is summarized.http://www.thieme-connect.de/DOI/DOI?10.4103/2277-9167.138924cervical myelopathyhand wastinghirayama diseasemagnetic resonance imaging
collection DOAJ
language English
format Article
sources DOAJ
author Chanabasappa V. Chavadi
Gowtham Jasti
Madhav Hegde
Anand Venugopal
spellingShingle Chanabasappa V. Chavadi
Gowtham Jasti
Madhav Hegde
Anand Venugopal
Hirayama disease
Indian Journal of Neurosurgery
cervical myelopathy
hand wasting
hirayama disease
magnetic resonance imaging
author_facet Chanabasappa V. Chavadi
Gowtham Jasti
Madhav Hegde
Anand Venugopal
author_sort Chanabasappa V. Chavadi
title Hirayama disease
title_short Hirayama disease
title_full Hirayama disease
title_fullStr Hirayama disease
title_full_unstemmed Hirayama disease
title_sort hirayama disease
publisher Thieme Medical Publishers, Inc.
series Indian Journal of Neurosurgery
issn 2277-954X
2277-9167
publishDate 2014-05-01
description Hirayama disease (HD) is a rare cause of cervical myelopathy often misdiagnosed as motor neuron disease and easily missed on routine magnetic resonance imaging (MRI), at time where detection is crucial to prevent irreversible cord injury. Believed to be a cervical flexion myelopathy, HD differs from motor neuron diseases because of its nonprogressive course and pathologic findings of chronic microcirculatory changes in the lower cervical cord. Dynamic forward displacement of dura in flexion causes asymmetric flattening of lower cervical cord. While dynamic contrast MRI is diagnostic, routine study has high predictive value. A case of HD, etiopathogenesis, imaging and treatment is summarized.
topic cervical myelopathy
hand wasting
hirayama disease
magnetic resonance imaging
url http://www.thieme-connect.de/DOI/DOI?10.4103/2277-9167.138924
work_keys_str_mv AT chanabasappavchavadi hirayamadisease
AT gowthamjasti hirayamadisease
AT madhavhegde hirayamadisease
AT anandvenugopal hirayamadisease
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