Embryonal rhabdomyosarcoma of the urachal ligament presenting as small bowel obstruction: Case report and review of the literature

Pediatric soft tissue sarcomas comprise a small proportion of pediatric solid malignancies and may arise in numerous anatomic locations such as the head and neck, trunk, extremities, and the genitourinary tract. Here, we present a case of rhabdomyosarcoma (RMS) arising from an unusual location, the...

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Main Authors: Imad Aljabban, Christa N. Grant
Format: Article
Language:English
Published: Elsevier 2020-02-01
Series:Journal of Pediatric Surgery Case Reports
Online Access:http://www.sciencedirect.com/science/article/pii/S2213576619303471
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spelling doaj-ddbdbd3bd8d94963b333c61486713a302020-11-25T02:19:35ZengElsevierJournal of Pediatric Surgery Case Reports2213-57662020-02-0153Embryonal rhabdomyosarcoma of the urachal ligament presenting as small bowel obstruction: Case report and review of the literatureImad Aljabban0Christa N. Grant1Pennsylvania State University College of Medicine, Hershey, PA, USAPennsylvania State University College of Medicine, Hershey, PA, USA; Penn State Health Milton S. Hershey Medical Center, Division of Pediatric Surgery, Hershey, PA, USA; Corresponding author. Pennsylvania State University College of Medicine, Hershey, PA, USA.Pediatric soft tissue sarcomas comprise a small proportion of pediatric solid malignancies and may arise in numerous anatomic locations such as the head and neck, trunk, extremities, and the genitourinary tract. Here, we present a case of rhabdomyosarcoma (RMS) arising from an unusual location, the urachus. The 3-year-old patient initially presented with signs of small bowel obstruction. On diagnostic laparoscopy, an infraumbilical mass was discovered and removed by laparotomy. Analysis of the specimen confirmed embryonal RMS (ERMS). The patient was treated with a regimen of postoperative chemotherapy and radiation therapy. Although rare, prompt diagnostic evaluation and treatment of RMS may improve the long-term morbidity and mortality of these patients.http://www.sciencedirect.com/science/article/pii/S2213576619303471
collection DOAJ
language English
format Article
sources DOAJ
author Imad Aljabban
Christa N. Grant
spellingShingle Imad Aljabban
Christa N. Grant
Embryonal rhabdomyosarcoma of the urachal ligament presenting as small bowel obstruction: Case report and review of the literature
Journal of Pediatric Surgery Case Reports
author_facet Imad Aljabban
Christa N. Grant
author_sort Imad Aljabban
title Embryonal rhabdomyosarcoma of the urachal ligament presenting as small bowel obstruction: Case report and review of the literature
title_short Embryonal rhabdomyosarcoma of the urachal ligament presenting as small bowel obstruction: Case report and review of the literature
title_full Embryonal rhabdomyosarcoma of the urachal ligament presenting as small bowel obstruction: Case report and review of the literature
title_fullStr Embryonal rhabdomyosarcoma of the urachal ligament presenting as small bowel obstruction: Case report and review of the literature
title_full_unstemmed Embryonal rhabdomyosarcoma of the urachal ligament presenting as small bowel obstruction: Case report and review of the literature
title_sort embryonal rhabdomyosarcoma of the urachal ligament presenting as small bowel obstruction: case report and review of the literature
publisher Elsevier
series Journal of Pediatric Surgery Case Reports
issn 2213-5766
publishDate 2020-02-01
description Pediatric soft tissue sarcomas comprise a small proportion of pediatric solid malignancies and may arise in numerous anatomic locations such as the head and neck, trunk, extremities, and the genitourinary tract. Here, we present a case of rhabdomyosarcoma (RMS) arising from an unusual location, the urachus. The 3-year-old patient initially presented with signs of small bowel obstruction. On diagnostic laparoscopy, an infraumbilical mass was discovered and removed by laparotomy. Analysis of the specimen confirmed embryonal RMS (ERMS). The patient was treated with a regimen of postoperative chemotherapy and radiation therapy. Although rare, prompt diagnostic evaluation and treatment of RMS may improve the long-term morbidity and mortality of these patients.
url http://www.sciencedirect.com/science/article/pii/S2213576619303471
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AT christangrant embryonalrhabdomyosarcomaoftheurachalligamentpresentingassmallbowelobstructioncasereportandreviewoftheliterature
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