An extremely rare elderly case of proximal epithelioid sarcoma of the vulva: case report with a review of literatures

• Main Authors: Si Eun Jeon, Jina Lee, Hee Jung Jung, Beob-Jong Kim, Sang-Young Ryu, Sang-Il Park, Hye-Sil Seol, Won-Il Jang, Moon-Hong Kim
• Format: Article
• Language: English
• Published: Korean Society of Obstetrics and Gynecology 2020-09-01
• Series: Obstetrics & Gynecology Science
• Subjects: vulva; vulvar neoplasms; sarcoma; immunohistochemistry; diagnosis, differential
• Online Access: http://www.ogscience.org/upload/pdf/ogs-20076.pdf

We experienced an extremely rare case of proximal epithelioid sarcoma (PES) of the vulva in a 77-year-old woman. After history taking and physical examination, the patient was tentatively diagnosed as having Bartholin’s cyst in the right labium. Based on histopathological and immunohistochemical (IHC) findings, however, a final diagnosis of PES of the vulva was made. After receiving CyberKnife treatment, the patient survived but with recurrent episodes and poor prognosis. In conclusion, our case indicates that patients with PES of the vulva should be appropriately managed with radiotherapy after a differential diagnosis based on histopathological and IHC findings.