Ebstein’s Anomaly, Left Ventricular Noncompaction, and Sudden Cardiac Death

Ebstein’s anomaly is a congenital disorder characterized by apical displacement of the septal leaflet of the tricuspid valve. Ebstein’s anomaly may be seen in association with other cardiac conditions, including patent foramen ovale, atrial septal defect, and left ventricular noncompaction (LVNC)....

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Main Authors: Michael McGee, Luke Warner, Nicholas Collins
Format: Article
Language:English
Published: Hindawi Limited 2015-01-01
Series:Case Reports in Cardiology
Online Access:http://dx.doi.org/10.1155/2015/854236
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spelling doaj-db18d9399b554db9989309ed546526de2020-11-24T22:26:01ZengHindawi LimitedCase Reports in Cardiology2090-64042090-64122015-01-01201510.1155/2015/854236854236Ebstein’s Anomaly, Left Ventricular Noncompaction, and Sudden Cardiac DeathMichael McGee0Luke Warner1Nicholas Collins2Cardiovascular Unit, John Hunter Hospital, Newcastle, NSW 2305, AustraliaCardiovascular Unit, John Hunter Hospital, Newcastle, NSW 2305, AustraliaCardiovascular Unit, John Hunter Hospital, Newcastle, NSW 2305, AustraliaEbstein’s anomaly is a congenital disorder characterized by apical displacement of the septal leaflet of the tricuspid valve. Ebstein’s anomaly may be seen in association with other cardiac conditions, including patent foramen ovale, atrial septal defect, and left ventricular noncompaction (LVNC). LVNC is characterized by increased trabeculation within the left ventricular apex. Echocardiography is often used to diagnose LVNC; however, magnetic resonance (MR) imaging offers superior characterization of the myocardium. We report a case of sudden cardiac death in a patient with Ebstein’s anomaly with unrecognized LVNC noted on post mortem examination with screening documenting the presence of LVNC in one of the patient’s twin sons.http://dx.doi.org/10.1155/2015/854236
collection DOAJ
language English
format Article
sources DOAJ
author Michael McGee
Luke Warner
Nicholas Collins
spellingShingle Michael McGee
Luke Warner
Nicholas Collins
Ebstein’s Anomaly, Left Ventricular Noncompaction, and Sudden Cardiac Death
Case Reports in Cardiology
author_facet Michael McGee
Luke Warner
Nicholas Collins
author_sort Michael McGee
title Ebstein’s Anomaly, Left Ventricular Noncompaction, and Sudden Cardiac Death
title_short Ebstein’s Anomaly, Left Ventricular Noncompaction, and Sudden Cardiac Death
title_full Ebstein’s Anomaly, Left Ventricular Noncompaction, and Sudden Cardiac Death
title_fullStr Ebstein’s Anomaly, Left Ventricular Noncompaction, and Sudden Cardiac Death
title_full_unstemmed Ebstein’s Anomaly, Left Ventricular Noncompaction, and Sudden Cardiac Death
title_sort ebstein’s anomaly, left ventricular noncompaction, and sudden cardiac death
publisher Hindawi Limited
series Case Reports in Cardiology
issn 2090-6404
2090-6412
publishDate 2015-01-01
description Ebstein’s anomaly is a congenital disorder characterized by apical displacement of the septal leaflet of the tricuspid valve. Ebstein’s anomaly may be seen in association with other cardiac conditions, including patent foramen ovale, atrial septal defect, and left ventricular noncompaction (LVNC). LVNC is characterized by increased trabeculation within the left ventricular apex. Echocardiography is often used to diagnose LVNC; however, magnetic resonance (MR) imaging offers superior characterization of the myocardium. We report a case of sudden cardiac death in a patient with Ebstein’s anomaly with unrecognized LVNC noted on post mortem examination with screening documenting the presence of LVNC in one of the patient’s twin sons.
url http://dx.doi.org/10.1155/2015/854236
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