Stiff Person Syndrome Associated with Compartment Syndrome

Stiff person syndrome (SPS) is a rare and disabling neurological disorder of autoimmune origin, characterized by progressive stiffness and muscle spasms affecting the axial and limb muscles, most frequently associated with antibodies against glutamic acid decarboxylase. We describe a patient who pre...

Full description

Bibliographic Details
Main Authors:	Kok Pin Yong, Yew Long Lo
Format:	Article
Language:	English
Published:	Karger Publishers 2019-07-01
Series:	Case Reports in Neurology
Subjects:	Stiff person syndrome Compartment syndrome Glutamic acid decarboxylase antibody Autoimmune disease
Online Access:	https://www.karger.com/Article/FullText/501793

id	doaj-dac11cc980104d4a8e81cf9dd8d54969
record_format	Article
spelling	doaj-dac11cc980104d4a8e81cf9dd8d549692020-11-25T00:46:44ZengKarger PublishersCase Reports in Neurology1662-680X2019-07-0111221722110.1159/000501793501793Stiff Person Syndrome Associated with Compartment SyndromeKok Pin YongYew Long LoStiff person syndrome (SPS) is a rare and disabling neurological disorder of autoimmune origin, characterized by progressive stiffness and muscle spasms affecting the axial and limb muscles, most frequently associated with antibodies against glutamic acid decarboxylase. We describe a patient who presented initially with compartment syndrome and was later diagnosed with SPS.This is the first case report of SPS possibly presenting initially with compartment syndrome. This case illustrates the importance of recognizing that patients with SPS may present with varied manifestations, including compartment syndrome, which by itself is a medical emergency.https://www.karger.com/Article/FullText/501793Stiff person syndromeCompartment syndromeGlutamic acid decarboxylase antibodyAutoimmune disease
collection	DOAJ
language	English
format	Article
sources	DOAJ
author	Kok Pin Yong Yew Long Lo
spellingShingle	Kok Pin Yong Yew Long Lo Stiff Person Syndrome Associated with Compartment Syndrome Case Reports in Neurology Stiff person syndrome Compartment syndrome Glutamic acid decarboxylase antibody Autoimmune disease
author_facet	Kok Pin Yong Yew Long Lo
author_sort	Kok Pin Yong
title	Stiff Person Syndrome Associated with Compartment Syndrome
title_short	Stiff Person Syndrome Associated with Compartment Syndrome
title_full	Stiff Person Syndrome Associated with Compartment Syndrome
title_fullStr	Stiff Person Syndrome Associated with Compartment Syndrome
title_full_unstemmed	Stiff Person Syndrome Associated with Compartment Syndrome
title_sort	stiff person syndrome associated with compartment syndrome
publisher	Karger Publishers
series	Case Reports in Neurology
issn	1662-680X
publishDate	2019-07-01
description	Stiff person syndrome (SPS) is a rare and disabling neurological disorder of autoimmune origin, characterized by progressive stiffness and muscle spasms affecting the axial and limb muscles, most frequently associated with antibodies against glutamic acid decarboxylase. We describe a patient who presented initially with compartment syndrome and was later diagnosed with SPS.This is the first case report of SPS possibly presenting initially with compartment syndrome. This case illustrates the importance of recognizing that patients with SPS may present with varied manifestations, including compartment syndrome, which by itself is a medical emergency.
topic	Stiff person syndrome Compartment syndrome Glutamic acid decarboxylase antibody Autoimmune disease
url	https://www.karger.com/Article/FullText/501793
work_keys_str_mv	AT kokpinyong stiffpersonsyndromeassociatedwithcompartmentsyndrome AT yewlonglo stiffpersonsyndromeassociatedwithcompartmentsyndrome
_version_	1725263485551509504

Stiff Person Syndrome Associated with Compartment Syndrome

Similar Items