Extraskeletal Ewing’s sarcoma/peripheral primitive neuroectodermal tumor of the small bowel presenting with gastrointestinal perforation
Vipul D Yagnik,1 Sushil Dawka21Department of Surgical Gastroenterology, Nishtha surgical hospital and research center, Patan, Gujarat, India; 2Department of surgery, SSR Medical College, Belle Rive, MauritiusAbstract: Extraskeletal Ewing’s sarcoma (E-EWS)/peripheral primitive neuroectoderm...
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doaj-da0e2f9066bc438ba3fe37d74b261b1a2020-11-25T02:22:45ZengDove Medical PressClinical and Experimental Gastroenterology1178-70232019-06-01Volume 1227928546634Extraskeletal Ewing’s sarcoma/peripheral primitive neuroectodermal tumor of the small bowel presenting with gastrointestinal perforationYagnik VDDawka SVipul D Yagnik,1 Sushil Dawka21Department of Surgical Gastroenterology, Nishtha surgical hospital and research center, Patan, Gujarat, India; 2Department of surgery, SSR Medical College, Belle Rive, MauritiusAbstract: Extraskeletal Ewing’s sarcoma (E-EWS)/peripheral primitive neuroectodermal tumor (pPNET) is a rare soft tissue tumor that arises from a multipotent progenitor cell and is considered to be of neuroectodermal origin. Although soft tissue E-EWS/pPNETs are common, they are exceedingly rare in the small bowel. Only 30 cases of E-EWS/pPNET of the small bowel have been reported. However, only one case of gastrointestinal perforation has been reported till today. Here, we report the second case of E- EWS/pPNET with gastrointestinal perforation.Keywords: peripheral primitive neuroectodermal tumor, immunohistochemistry, gastrointestinal perforation, surgery, chemotherapyhttps://www.dovepress.com/extraskeletal-ewings-sarcoma-peripheral-primitive-neuroectodermal-tumo-peer-reviewed-article-CEGperipheral primitive neuroectodermal tumorImmunohistochemistryGastrointestinal perforationSurgeryChemotherapy |
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DOAJ |
language |
English |
format |
Article |
sources |
DOAJ |
author |
Yagnik VD Dawka S |
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Yagnik VD Dawka S Extraskeletal Ewing’s sarcoma/peripheral primitive neuroectodermal tumor of the small bowel presenting with gastrointestinal perforation Clinical and Experimental Gastroenterology peripheral primitive neuroectodermal tumor Immunohistochemistry Gastrointestinal perforation Surgery Chemotherapy |
author_facet |
Yagnik VD Dawka S |
author_sort |
Yagnik VD |
title |
Extraskeletal Ewing’s sarcoma/peripheral primitive neuroectodermal tumor of the small bowel presenting with gastrointestinal perforation |
title_short |
Extraskeletal Ewing’s sarcoma/peripheral primitive neuroectodermal tumor of the small bowel presenting with gastrointestinal perforation |
title_full |
Extraskeletal Ewing’s sarcoma/peripheral primitive neuroectodermal tumor of the small bowel presenting with gastrointestinal perforation |
title_fullStr |
Extraskeletal Ewing’s sarcoma/peripheral primitive neuroectodermal tumor of the small bowel presenting with gastrointestinal perforation |
title_full_unstemmed |
Extraskeletal Ewing’s sarcoma/peripheral primitive neuroectodermal tumor of the small bowel presenting with gastrointestinal perforation |
title_sort |
extraskeletal ewing’s sarcoma/peripheral primitive neuroectodermal tumor of the small bowel presenting with gastrointestinal perforation |
publisher |
Dove Medical Press |
series |
Clinical and Experimental Gastroenterology |
issn |
1178-7023 |
publishDate |
2019-06-01 |
description |
Vipul D Yagnik,1 Sushil Dawka21Department of Surgical Gastroenterology, Nishtha surgical hospital and research center, Patan, Gujarat, India; 2Department of surgery, SSR Medical College, Belle Rive, MauritiusAbstract: Extraskeletal Ewing’s sarcoma (E-EWS)/peripheral primitive neuroectodermal tumor (pPNET) is a rare soft tissue tumor that arises from a multipotent progenitor cell and is considered to be of neuroectodermal origin. Although soft tissue E-EWS/pPNETs are common, they are exceedingly rare in the small bowel. Only 30 cases of E-EWS/pPNET of the small bowel have been reported. However, only one case of gastrointestinal perforation has been reported till today. Here, we report the second case of E- EWS/pPNET with gastrointestinal perforation.Keywords: peripheral primitive neuroectodermal tumor, immunohistochemistry, gastrointestinal perforation, surgery, chemotherapy |
topic |
peripheral primitive neuroectodermal tumor Immunohistochemistry Gastrointestinal perforation Surgery Chemotherapy |
url |
https://www.dovepress.com/extraskeletal-ewings-sarcoma-peripheral-primitive-neuroectodermal-tumo-peer-reviewed-article-CEG |
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