Extraskeletal Ewing’s sarcoma/peripheral primitive neuroectodermal tumor of the small bowel presenting with gastrointestinal perforation

Vipul D Yagnik,1 Sushil Dawka21Department of Surgical Gastroenterology, Nishtha surgical hospital and research center, Patan, Gujarat, India; 2Department of surgery, SSR Medical College, Belle Rive, MauritiusAbstract: Extraskeletal Ewing’s sarcoma (E-EWS)/peripheral primitive neuroectoderm...

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Main Authors: Yagnik VD, Dawka S
Format: Article
Language:English
Published: Dove Medical Press 2019-06-01
Series:Clinical and Experimental Gastroenterology
Subjects:
Online Access:https://www.dovepress.com/extraskeletal-ewings-sarcoma-peripheral-primitive-neuroectodermal-tumo-peer-reviewed-article-CEG
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spelling doaj-da0e2f9066bc438ba3fe37d74b261b1a2020-11-25T02:22:45ZengDove Medical PressClinical and Experimental Gastroenterology1178-70232019-06-01Volume 1227928546634Extraskeletal Ewing’s sarcoma/peripheral primitive neuroectodermal tumor of the small bowel presenting with gastrointestinal perforationYagnik VDDawka SVipul D Yagnik,1 Sushil Dawka21Department of Surgical Gastroenterology, Nishtha surgical hospital and research center, Patan, Gujarat, India; 2Department of surgery, SSR Medical College, Belle Rive, MauritiusAbstract: Extraskeletal Ewing’s sarcoma (E-EWS)/peripheral primitive neuroectodermal tumor (pPNET) is a rare soft tissue tumor that arises from a multipotent progenitor cell and is considered to be of neuroectodermal origin. Although soft tissue E-EWS/pPNETs are common, they are exceedingly rare in the small bowel. Only 30 cases of E-EWS/pPNET of the small bowel have been reported. However, only one case of gastrointestinal perforation has been reported till today. Here, we report the second case of E- EWS/pPNET with gastrointestinal perforation.Keywords: peripheral primitive neuroectodermal tumor, immunohistochemistry, gastrointestinal perforation, surgery, chemotherapyhttps://www.dovepress.com/extraskeletal-ewings-sarcoma-peripheral-primitive-neuroectodermal-tumo-peer-reviewed-article-CEGperipheral primitive neuroectodermal tumorImmunohistochemistryGastrointestinal perforationSurgeryChemotherapy
collection DOAJ
language English
format Article
sources DOAJ
author Yagnik VD
Dawka S
spellingShingle Yagnik VD
Dawka S
Extraskeletal Ewing’s sarcoma/peripheral primitive neuroectodermal tumor of the small bowel presenting with gastrointestinal perforation
Clinical and Experimental Gastroenterology
peripheral primitive neuroectodermal tumor
Immunohistochemistry
Gastrointestinal perforation
Surgery
Chemotherapy
author_facet Yagnik VD
Dawka S
author_sort Yagnik VD
title Extraskeletal Ewing’s sarcoma/peripheral primitive neuroectodermal tumor of the small bowel presenting with gastrointestinal perforation
title_short Extraskeletal Ewing’s sarcoma/peripheral primitive neuroectodermal tumor of the small bowel presenting with gastrointestinal perforation
title_full Extraskeletal Ewing’s sarcoma/peripheral primitive neuroectodermal tumor of the small bowel presenting with gastrointestinal perforation
title_fullStr Extraskeletal Ewing’s sarcoma/peripheral primitive neuroectodermal tumor of the small bowel presenting with gastrointestinal perforation
title_full_unstemmed Extraskeletal Ewing’s sarcoma/peripheral primitive neuroectodermal tumor of the small bowel presenting with gastrointestinal perforation
title_sort extraskeletal ewing’s sarcoma/peripheral primitive neuroectodermal tumor of the small bowel presenting with gastrointestinal perforation
publisher Dove Medical Press
series Clinical and Experimental Gastroenterology
issn 1178-7023
publishDate 2019-06-01
description Vipul D Yagnik,1 Sushil Dawka21Department of Surgical Gastroenterology, Nishtha surgical hospital and research center, Patan, Gujarat, India; 2Department of surgery, SSR Medical College, Belle Rive, MauritiusAbstract: Extraskeletal Ewing’s sarcoma (E-EWS)/peripheral primitive neuroectodermal tumor (pPNET) is a rare soft tissue tumor that arises from a multipotent progenitor cell and is considered to be of neuroectodermal origin. Although soft tissue E-EWS/pPNETs are common, they are exceedingly rare in the small bowel. Only 30 cases of E-EWS/pPNET of the small bowel have been reported. However, only one case of gastrointestinal perforation has been reported till today. Here, we report the second case of E- EWS/pPNET with gastrointestinal perforation.Keywords: peripheral primitive neuroectodermal tumor, immunohistochemistry, gastrointestinal perforation, surgery, chemotherapy
topic peripheral primitive neuroectodermal tumor
Immunohistochemistry
Gastrointestinal perforation
Surgery
Chemotherapy
url https://www.dovepress.com/extraskeletal-ewings-sarcoma-peripheral-primitive-neuroectodermal-tumo-peer-reviewed-article-CEG
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AT dawkas extraskeletalewingrsquossarcomaperipheralprimitiveneuroectodermaltumorofthesmallbowelpresentingwithgastrointestinalperforation
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