Extraskeletal Ewing’s sarcoma/peripheral primitive neuroectodermal tumor of the small bowel presenting with gastrointestinal perforation

• Main Authors: Yagnik VD, Dawka S
• Format: Article
• Language: English
• Published: Dove Medical Press 2019-06-01
• Series: Clinical and Experimental Gastroenterology
• Subjects: peripheral primitive neuroectodermal tumor; Immunohistochemistry; Gastrointestinal perforation; Surgery; Chemotherapy
• Online Access: https://www.dovepress.com/extraskeletal-ewings-sarcoma-peripheral-primitive-neuroectodermal-tumo-peer-reviewed-article-CEG
• ISSN: 1178-7023

Vipul D Yagnik,1 Sushil Dawka21Department of Surgical Gastroenterology, Nishtha surgical hospital and research center, Patan, Gujarat, India; 2Department of surgery, SSR Medical College, Belle Rive, MauritiusAbstract: Extraskeletal Ewing’s sarcoma (E-EWS)/peripheral primitive neuroectodermal tumor (pPNET) is a rare soft tissue tumor that arises from a multipotent progenitor cell and is considered to be of neuroectodermal origin. Although soft tissue E-EWS/pPNETs are common, they are exceedingly rare in the small bowel. Only 30 cases of E-EWS/pPNET of the small bowel have been reported. However, only one case of gastrointestinal perforation has been reported till today. Here, we report the second case of E- EWS/pPNET with gastrointestinal perforation.Keywords: peripheral primitive neuroectodermal tumor, immunohistochemistry, gastrointestinal perforation, surgery, chemotherapy