Facial plexiform neurofibroma in a child with neurofibromatosis type I: A case report

Facial plexiform neurofibroma in a child with neurofibromatosis type I: A case report

Plexiform neurofibroma is a non-circumscribed, thick, and irregular benign tumor of the peripheral nerve sheath. It is a virtually pathognomonic and often disabling feature of neurofibromatosis type I. The diffuse and soft nature of plexiform neurofibroma is often compared to ′a bag of wo...

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Bibliographic Details
Main Authors: Patil K, Mahima V, Shetty S, Lahari K
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2007-03-01
Series:Journal of Indian Society of Pedodontics and Preventive Dentistry
Subjects:
Bag of worms
cafι au lait macules
neurofibromatosis type-I
plexiform neurofibroma
von Recklinghausen′s disease
Online Access:http://www.jisppd.com/article.asp?issn=0970-4388;year=2007;volume=25;issue=1;spage=30;epage=35;aulast=Patil
Description
Summary:Plexiform neurofibroma is a non-circumscribed, thick, and irregular benign tumor of the peripheral nerve sheath. It is a virtually pathognomonic and often disabling feature of neurofibromatosis type I. The diffuse and soft nature of plexiform neurofibroma is often compared to ′a bag of worms′ and is difficult to distinguish from a vascular malformation or a lymphangioma, thus necessitating thorough clinical and histopathological examination and imaging of the lesion. We present a case of plexiform neurofibroma in a 12-year-old male child.
ISSN:0970-4388

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