Hypoglossal neuropathology and respiratory activity in Pompe mice

Hypoglossal neuropathology and respiratory activity in Pompe mice

Pompe disease is a lysosomal storage disorder associated with systemic deficiency of acid α-glucosidase (GAA). Respiratory-related problems in Pompe disease include hypoventilation and upper airway dysfunction. Although these problems have generally been attributed to muscular pathology, recent wo...

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Bibliographic Details
Main Authors: Kun-Ze eLee, Kai eQiu, Milapjit S Sandhu, Mai K Elmallah, Darin J Falk, Michael A Lane, Paul J Reier, Barry J Byrne, David D Fuller
Format: Article
Language:English
Published: Frontiers Media S.A. 2011-06-01
Series:Frontiers in Physiology
Subjects:
Glycogen
brainstem
hypoglossal
acid alpha-glucosidase
Pompe
Online Access:http://journal.frontiersin.org/Journal/10.3389/fphys.2011.00031/full

Internet

http://journal.frontiersin.org/Journal/10.3389/fphys.2011.00031/full

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