A Drosophila model for the Zellweger spectrum of peroxisome biogenesis disorders
SUMMARY Human peroxisome biogenesis disorders are lethal genetic diseases in which abnormal peroxisome assembly compromises overall peroxisome and cellular function. Peroxisomes are ubiquitous membrane-bound organelles involved in several important biochemical processes, notably lipid metabolism and...
Main Authors: | , , , , , |
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Format: | Article |
Language: | English |
Published: |
The Company of Biologists
2011-09-01
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Series: | Disease Models & Mechanisms |
Online Access: | http://dmm.biologists.org/content/4/5/659 |