Recurrence of Primary Vascular Leiomyosarcoma Five Years after Initial Diagnosis in the Lower Extremity

Primary leiomyosarcomas of vascular origin are rare tumors. They frequently arise within the inferior vena cava; however, the peripheral vein was also affected. To date, only a few hundred cases have been reported in the world literature. Although it is an extremely aggressive tumor, the symptoms ma...

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Main Authors: Hilal Erinanc, Mehmet Ozulku, Aysen Terzi
Format: Article
Language:English
Published: Hindawi Limited 2018-01-01
Series:Case Reports in Oncological Medicine
Online Access:http://dx.doi.org/10.1155/2018/3094616
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spelling doaj-d41b4d77acc5457e8d1a50a30fd731062020-11-25T00:55:02ZengHindawi LimitedCase Reports in Oncological Medicine2090-67062090-67142018-01-01201810.1155/2018/30946163094616Recurrence of Primary Vascular Leiomyosarcoma Five Years after Initial Diagnosis in the Lower ExtremityHilal Erinanc0Mehmet Ozulku1Aysen Terzi2Konya Uygulama ve Arastırma Hastanesi, Pathology Department, Medicine Faculty, Baskent University, Selcuklu, Konya, TurkeyKonya Uygulama ve Arastırma Hastanesi, Cardiothoracic Surgery Department, Medicine Faculty, Baskent University, Selcuklu, Konya, TurkeyPathology Department, Medicine Faculty, Baskent University, Ankara, TurkeyPrimary leiomyosarcomas of vascular origin are rare tumors. They frequently arise within the inferior vena cava; however, the peripheral vein was also affected. To date, only a few hundred cases have been reported in the world literature. Although it is an extremely aggressive tumor, the symptoms may be unspecific, especially in the lower extremities. In this report, we present a case of primary vascular leiomyosarcoma, arising from the short saphenous vein, with symptoms mimicking thrombus in the initial diagnosis. The diagnosis of leiomyosarcomas was confirmed by standard H&E staining and immunohistochemical staining. Recurrence of the tumor has been observed five years after surgical treatment. Due to its rarity, experience in the management of this type of tumor is limited. The mainstay of treatment for these tumors is complete surgical resection. The purpose of the presented case is to discuss the clinicopathological features and management options of this tumor, under the light of the most recent literatures.http://dx.doi.org/10.1155/2018/3094616
collection DOAJ
language English
format Article
sources DOAJ
author Hilal Erinanc
Mehmet Ozulku
Aysen Terzi
spellingShingle Hilal Erinanc
Mehmet Ozulku
Aysen Terzi
Recurrence of Primary Vascular Leiomyosarcoma Five Years after Initial Diagnosis in the Lower Extremity
Case Reports in Oncological Medicine
author_facet Hilal Erinanc
Mehmet Ozulku
Aysen Terzi
author_sort Hilal Erinanc
title Recurrence of Primary Vascular Leiomyosarcoma Five Years after Initial Diagnosis in the Lower Extremity
title_short Recurrence of Primary Vascular Leiomyosarcoma Five Years after Initial Diagnosis in the Lower Extremity
title_full Recurrence of Primary Vascular Leiomyosarcoma Five Years after Initial Diagnosis in the Lower Extremity
title_fullStr Recurrence of Primary Vascular Leiomyosarcoma Five Years after Initial Diagnosis in the Lower Extremity
title_full_unstemmed Recurrence of Primary Vascular Leiomyosarcoma Five Years after Initial Diagnosis in the Lower Extremity
title_sort recurrence of primary vascular leiomyosarcoma five years after initial diagnosis in the lower extremity
publisher Hindawi Limited
series Case Reports in Oncological Medicine
issn 2090-6706
2090-6714
publishDate 2018-01-01
description Primary leiomyosarcomas of vascular origin are rare tumors. They frequently arise within the inferior vena cava; however, the peripheral vein was also affected. To date, only a few hundred cases have been reported in the world literature. Although it is an extremely aggressive tumor, the symptoms may be unspecific, especially in the lower extremities. In this report, we present a case of primary vascular leiomyosarcoma, arising from the short saphenous vein, with symptoms mimicking thrombus in the initial diagnosis. The diagnosis of leiomyosarcomas was confirmed by standard H&E staining and immunohistochemical staining. Recurrence of the tumor has been observed five years after surgical treatment. Due to its rarity, experience in the management of this type of tumor is limited. The mainstay of treatment for these tumors is complete surgical resection. The purpose of the presented case is to discuss the clinicopathological features and management options of this tumor, under the light of the most recent literatures.
url http://dx.doi.org/10.1155/2018/3094616
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AT mehmetozulku recurrenceofprimaryvascularleiomyosarcomafiveyearsafterinitialdiagnosisinthelowerextremity
AT aysenterzi recurrenceofprimaryvascularleiomyosarcomafiveyearsafterinitialdiagnosisinthelowerextremity
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