Cerebral and occipito-atlanto-axial involvement in mucopolysaccharidosis patients: clinical, radiological, and neurosurgical features

Cerebral and occipito-atlanto-axial involvement in mucopolysaccharidosis patients: clinical, radiological, and neurosurgical features

Abstract Background Neurosurgical features of mucopolysaccharidosis (MPS) patients mainly involve the presence of cranio-vertebral junction (CVJ) abnormalities and the development of communicating hydrocephalus. CVJ pathology is a critical aspect that severely influences the morbidity and mortality...

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Bibliographic Details
Main Authors: Carlo Giussani, Lelio Guida, Francesco Canonico, Erik P. Sganzerla
Format: Article
Language:English
Published: BMC 2018-11-01
Series:Italian Journal of Pediatrics
Subjects:
Mucopolysaccharidosis
Craniovertebral junction instability
Hydrocephalus
Cerebral atrophy
Online Access:http://link.springer.com/article/10.1186/s13052-018-0558-x

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