Anaesthesic management in patients with epidermolysis bullosa

Epidermolysis bullosa (EB) is a rare genetic disease, characterized by blistering of skin and mucous membranes following minor trauma. Scar formation as well as systemic consequences (anemia, hypoproteinemia, cardiac disorders, cancer) are the hallmarks of disease. This case report describes a...

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Bibliographic Details
Main Authors: Sergeja Kozar, Sabina Štivan
Format: Article
Language:English
Published: Slovenian Medical Association 2012-08-01
Series:Zdravniški Vestnik
Online Access:http://vestnik.szd.si/index.php/ZdravVest/article/view/798
Description
Summary:Epidermolysis bullosa (EB) is a rare genetic disease, characterized by blistering of skin and mucous membranes following minor trauma. Scar formation as well as systemic consequences (anemia, hypoproteinemia, cardiac disorders, cancer) are the hallmarks of disease. This case report describes a 34-year-old patient with dystrophic form of EB, who required urgent surgical intervention due to arterial bleeding in the groin region. A detailed description of preoperative assessment, anaesthetic implications (monitoring, airway maintenance, general anaesthesia) as well as postoperative analgesia are discussed bellow.
ISSN:1318-0347
1581-0224