Peripheral Primitive Neuroectodermal Tumour of the Maxilla and Paranasal Sinuses: A Rare Clinical Presentation

• Main Authors: C.L. Krithika, S. Sathasivasubramanian, C. Ponranjini Vedeswari
• Format: Article
• Language: English
• Published: JCDR Research and Publications Private Limited 2015-05-01
• Series: Journal of Clinical and Diagnostic Research
• Subjects: aggressive; oral cavity; small round cell tumours
• Online Access: https://jcdr.net/articles/PDF/5949/13055_CE(RA1)_F(T)_PF1(AGAK)_PFA(AK)_PF2(PAG).pdf

Peripheral Primitive Neuroectodermal Tumours (pPNET) are rare aggressive tumours of neural crest cell origin. These tumours are more common in children and young adults. This is a unique report of one such presentation in a 23-year-old lady occurring in the left side posterior maxilla and Paranasal sinuses along with imaging characteristics, histopathologic features, immunohistochemical aspects and management. Though these tumours are rare, they should be considered in the differential diagnosis of rapidly growing soft tissue masses in young adults. Precise diagnosis with timely management is necessary for good prognosis.