Conventional (Adult Type) Hemangiopericytoma of Thigh in Association with Arteriovenous Malformation and Epidermal Inclusion Cyst: A Rare Combination, At an Unusual Site

• Main Authors: Neelam Sood, Kumar Sharad Sinha
• Format: Article
• Language: English
• Published: Krishna Institute of Medical Sciences University 2017-01-01
• Series: Journal of Krishna Institute of Medical Sciences University
• Subjects: Arteriovenous Malformation; Epidermal inclusion cyst; Hemangiopericytoma; Vascular lesion
• Online Access: http://www.jkimsu.com/jkimsu-vol6no1/JKIMSU,%20Vol.%206,%20No.%201,%20Jan-Mar%202017%20Page%20120-126.pdf
• ISSN: 2231-4261; 2231-4261

Hemangiopericytoma was first described in 1942 by Stout and Murray as a distinctive soft tissue neoplasm of pericytic orgin characterized by ‘staghorn’ branching pattern. It is no longer considered a specific entity but rather a growth pattern shared by many unrelated benign and malignant neoplasms. The pathogenesis of Areteriovenous malformations is not well understood. Rarely, it has been reported with associated arteriovenous malformations. We present a rare case of combination of Hemangiopericytoma with arteriovenous malformations and epidermal inclusion cyst in the same lesion in leg. A 62 year male patient presented with a polypoidal cutaneous growth over posterior aspect of right thigh measuring 8x8x5 cm for past 25 years, firm in consistency. Radiological features revealed an areteriovenous malformation with soft tissue attenuation vascular mass. Cytological findings of the swelling were suggestive of a vascular lesion with cystic degeneration. Excision of the mass was performed and specimen was received as a large skin covered polypoidal mass measuring 14x10x5 cm. To the best of our knowledge, no prior report mentions a tumour of this size, associated with arteriovenous malformation and epidermal inclusion cyst of lower extremity.