Bile acids: the role of peroxisomes

Bile acids: the role of peroxisomes

It is well established that peroxisomes play a crucial role in de novo bile acid synthesis. Studies in patients with a peroxisomal disorder have been indispensable for the elucidation of the precise role of peroxisomes. Several peroxisomal disorders are associated with distinct bile acid abnormaliti...

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Bibliographic Details
Main Authors:	Sacha Ferdinandusse, Simone Denis, Phyllis L. Faust, Ronald J.A. Wanders
Format:	Article
Language:	English
Published:	Elsevier 2009-11-01
Series:	Journal of Lipid Research
Subjects:	dihydroxycholestanoic acid trihydroxy-cholestanoic acid peroxisome deficiency disorders D-bifunctional protein deficiency α-methylacyl-CoA racemase deficiency
Online Access:	http://www.sciencedirect.com/science/article/pii/S0022227520306799

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