Idiopathic Pulmonary Hemosiderosis in a Child with Recurrent Macrophage Activation Syndrome Secondary to Systemic Juvenile Idiopathic Arthritis

Idiopathic Pulmonary Hemosiderosis in a Child with Recurrent Macrophage Activation Syndrome Secondary to Systemic Juvenile Idiopathic Arthritis

Macrophage activation syndrome, a severe complication of systemic juvenile idiopathic arthritis and other inflammatory diseases, represents one of the most important rheumatological emergencies. Delayed diagnosis could lead to life-threatening complications. Pulmonary hemosiderosis has been classica...

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Main Authors: Kenan Barut, Sezgin Sahin, Amra Adrovic, Velat Sen, Ozgur Kasapcopur
Format: Article
Language:English
Published: Hindawi Limited 2017-01-01
Series:Case Reports in Pediatrics
Online Access:http://dx.doi.org/10.1155/2017/5693501
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spelling doaj-c7c89e8964c34a52ae5443c5c78f23e22020-11-24T23:00:03ZengHindawi LimitedCase Reports in Pediatrics2090-68032090-68112017-01-01201710.1155/2017/56935015693501Idiopathic Pulmonary Hemosiderosis in a Child with Recurrent Macrophage Activation Syndrome Secondary to Systemic Juvenile Idiopathic ArthritisKenan Barut0Sezgin Sahin1Amra Adrovic2Velat Sen3Ozgur Kasapcopur4Department of Pediatric Rheumatology, Cerrahpasa Medical School, Istanbul University, Istanbul, TurkeyDepartment of Pediatric Rheumatology, Cerrahpasa Medical School, Istanbul University, Istanbul, TurkeyDepartment of Pediatric Rheumatology, Cerrahpasa Medical School, Istanbul University, Istanbul, TurkeyDepartment of Pediatric Chest Disease, Medical Faculty, Dicle University, Diyarbakir, TurkeyDepartment of Pediatric Rheumatology, Cerrahpasa Medical School, Istanbul University, Istanbul, TurkeyMacrophage activation syndrome, a severe complication of systemic juvenile idiopathic arthritis and other inflammatory diseases, represents one of the most important rheumatological emergencies. Delayed diagnosis could lead to life-threatening complications. Pulmonary hemosiderosis has been classically characterized by a triad of anemia, hemoptysis, and lung infiltrates on chest radiogram. Although the majority of patients of pulmonary hemosiderosis are considered idiopathic, secondary hemosiderosis associated with known diseases could be seen. In this case report, we aimed to present gradually increased pulmonary manifestations due to pulmonary hemosiderosis with recurrent macrophage activation syndrome attacks in a child with systemic juvenile idiopathic arthritis.http://dx.doi.org/10.1155/2017/5693501
collection DOAJ
language English
format Article
sources DOAJ
author Kenan Barut
Sezgin Sahin
Amra Adrovic
Velat Sen
Ozgur Kasapcopur
spellingShingle Kenan Barut
Sezgin Sahin
Amra Adrovic
Velat Sen
Ozgur Kasapcopur
Idiopathic Pulmonary Hemosiderosis in a Child with Recurrent Macrophage Activation Syndrome Secondary to Systemic Juvenile Idiopathic Arthritis
Case Reports in Pediatrics
author_facet Kenan Barut
Sezgin Sahin
Amra Adrovic
Velat Sen
Ozgur Kasapcopur
author_sort Kenan Barut
title Idiopathic Pulmonary Hemosiderosis in a Child with Recurrent Macrophage Activation Syndrome Secondary to Systemic Juvenile Idiopathic Arthritis
title_short Idiopathic Pulmonary Hemosiderosis in a Child with Recurrent Macrophage Activation Syndrome Secondary to Systemic Juvenile Idiopathic Arthritis
title_full Idiopathic Pulmonary Hemosiderosis in a Child with Recurrent Macrophage Activation Syndrome Secondary to Systemic Juvenile Idiopathic Arthritis
title_fullStr Idiopathic Pulmonary Hemosiderosis in a Child with Recurrent Macrophage Activation Syndrome Secondary to Systemic Juvenile Idiopathic Arthritis
title_full_unstemmed Idiopathic Pulmonary Hemosiderosis in a Child with Recurrent Macrophage Activation Syndrome Secondary to Systemic Juvenile Idiopathic Arthritis
title_sort idiopathic pulmonary hemosiderosis in a child with recurrent macrophage activation syndrome secondary to systemic juvenile idiopathic arthritis
publisher Hindawi Limited
series Case Reports in Pediatrics
issn 2090-6803
2090-6811
publishDate 2017-01-01
description Macrophage activation syndrome, a severe complication of systemic juvenile idiopathic arthritis and other inflammatory diseases, represents one of the most important rheumatological emergencies. Delayed diagnosis could lead to life-threatening complications. Pulmonary hemosiderosis has been classically characterized by a triad of anemia, hemoptysis, and lung infiltrates on chest radiogram. Although the majority of patients of pulmonary hemosiderosis are considered idiopathic, secondary hemosiderosis associated with known diseases could be seen. In this case report, we aimed to present gradually increased pulmonary manifestations due to pulmonary hemosiderosis with recurrent macrophage activation syndrome attacks in a child with systemic juvenile idiopathic arthritis.
url http://dx.doi.org/10.1155/2017/5693501
work_keys_str_mv AT kenanbarut idiopathicpulmonaryhemosiderosisinachildwithrecurrentmacrophageactivationsyndromesecondarytosystemicjuvenileidiopathicarthritis
AT sezginsahin idiopathicpulmonaryhemosiderosisinachildwithrecurrentmacrophageactivationsyndromesecondarytosystemicjuvenileidiopathicarthritis
AT amraadrovic idiopathicpulmonaryhemosiderosisinachildwithrecurrentmacrophageactivationsyndromesecondarytosystemicjuvenileidiopathicarthritis
AT velatsen idiopathicpulmonaryhemosiderosisinachildwithrecurrentmacrophageactivationsyndromesecondarytosystemicjuvenileidiopathicarthritis
AT ozgurkasapcopur idiopathicpulmonaryhemosiderosisinachildwithrecurrentmacrophageactivationsyndromesecondarytosystemicjuvenileidiopathicarthritis
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