Jadassohn Lewandowsky syndrome: Type 1 pachyonychia congenita

Jadassohn Lewandowsky syndrome: Type 1 pachyonychia congenita

Pachyonychia congenita (PC) is a rare, usually autosomal dominant, genodermatosis characterized by tetrad of wedge shaped nail hypertrophy, focal palmoplantar keratoderma, oral leucokeratosis and follicular hyperkeratosis due to mutation in either of the three keratin genes, KRT6, KRT16 and KRT17. C...

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Bibliographic Details
Main Authors:	Anup Kumar Tiwary, Dharmendra Kumar Mishra
Format:	Article
Language:	English
Published:	Our Dermatology Online 2017-01-01
Series:	Nasza Dermatologia Online
Subjects:	Jadassohn Lewandowsky syndrome; Nail hypertrophy; Pachyonychia congenita
Online Access:	http://www.odermatol.com/issue-in-html/2017-1-15-jadassohn/

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