Prevalence and course of disease after lung resection in primary ciliary dyskinesia: a cohort & nested case-control study

Abstract Background Lung resection is a controversial and understudied therapeutic modality in Primary Ciliary Dyskinesia (PCD). We assessed the prevalence of lung resection in PCD across countries and compared disease course in lobectomised and non-lobectomised patients. Methods In the internationa...

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Main Authors: Panayiotis Kouis, Myrofora Goutaki, Florian S. Halbeisen, Ifigeneia Gioti, Nicos Middleton, Israel Amirav, on behalf of the Israeli PCD Consortium, Angelo Barbato, on behalf of the Italian PCD Consortium, Laura Behan, Mieke Boon, Nagehan Emiralioglu, Eric G. Haarman, Bulent Karadag, Cordula Koerner-Rettberg, Romain Lazor, on behalf of the Swiss PCD Group, Michael R. Loebinger, Bernard Maitre, on behalf of the French Reference Centre for Rare Lung Diseases, Henryk Mazurek, Lucy Morgan, Kim Gjerum Nielsen, Heymut Omran, Ugur Özçelik, Mareike Price, Andrzej Pogorzelski, Deborah Snijders, on behalf of the PCD Italian Consortium, Guillaume Thouvenin, Claudius Werner, Zorica Zivkovic, Claudia E. Kuehni, Panayiotis K. Yiallouros
Format: Article
Language:English
Published: BMC 2019-09-01
Series:Respiratory Research
Subjects:
Online Access:http://link.springer.com/article/10.1186/s12931-019-1183-y