Transformation of dermatofibrosarcoma protuberans into a fibrosarcoma

• Main Authors: Mohamed Ali Sbai, Sofien Benzarti, Khaled Bouzaidi, Feten Sbei, Riadh Maalla
• Format: Article
• Language: English
• Published: Wolters Kluwer Medknow Publications 2016-01-01
• Series: Indian Journal of Dermatology
• Subjects: Dermatofibrosarcoma protuberans; fibrosarcoma; margin of safety; pathology; surgery
• Online Access: http://www.e-ijd.org/article.asp?issn=0019-5154;year=2016;volume=61;issue=1;spage=121;epage=121;aulast=Sbai

Dermatofibrosarcoma protuberans is a rare cutaneous mesenchymal tumor characterized by a low potential of malignancy with a very low rate of metastasis but an important rate of local recurrence. Its transformation into a fibrosarcoma is exceptional, responsible for a higher metastatic potential. This transformation implies a closer surveillance. Through a case report and literature review, we will try to expose epidemiological, clinical, histological, therapeutic, and outcome particularities of this entity.