Idiopathic pleuroparenchymal fibroelastosis: The first case to be managed with a successful lung transplant at King Faisal Specialist Hospital and Research Center, Riyadh

Idiopathic pleuroparenchymal fibroelastosis: The first case to be managed with a successful lung transplant at King Faisal Specialist Hospital and Research Center, Riyadh

Idiopathic Pleuro-Parenchymal Fibroelsatosis (PPFE) is a rare, progressive and recently recognized subtype of idiopathic interstitial lung disease with no recorded successful treatment other than lung transplant. We report a case of idiopathic pleuroparenchymal fibroelastosis from the Middle East, m...

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Bibliographic Details
Main Authors: Nour Abdullah Aljefri, Fayha Farraj Abothenain, Ahmed Mohamed Hussein, Waleed Saleh, Khaled Alkattan, Shamayel Faheem Mohammed, Mohammed Alhajji
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2019-01-01
Series:Annals of Thoracic Medicine
Subjects:
Interstitial lung disease
lung transplant
pleuroparenchymal fibroelastosis
Online Access:http://www.thoracicmedicine.org/article.asp?issn=1817-1737;year=2019;volume=14;issue=1;spage=94;epage=98;aulast=Aljefri
Description
Summary:Idiopathic Pleuro-Parenchymal Fibroelsatosis (PPFE) is a rare, progressive and recently recognized subtype of idiopathic interstitial lung disease with no recorded successful treatment other than lung transplant. We report a case of idiopathic pleuroparenchymal fibroelastosis from the Middle East, managed successfully by bilateral lung transplant performed on a 26 year old Saudi male.
ISSN:1817-1737
1998-3557

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